{"id":51,"date":"2023-11-06T10:45:02","date_gmt":"2023-11-06T10:45:02","guid":{"rendered":"https:\/\/liveunlimitedpku-dev-001.azurewebsites.net\/hu-hu\/?page_id=51"},"modified":"2024-12-07T20:24:57","modified_gmt":"2024-12-07T20:24:57","slug":"mi-a-pku","status":"publish","type":"page","link":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/mi-a-pku\/","title":{"rendered":"Mi a PKU?"},"content":{"rendered":"<div id=\"acf-block-6548d8e803832\" class=\"hero hero-no-overlay hero-large-first-para\">\n            <div class=\"hero-background-image hero-background-image-desktop\" style=\"background-image: url(https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-content\/uploads\/sites\/13\/2023\/11\/tup.png?v=0.74);\"><\/div>\n\t    <div class=\"hero-background-image hero-background-image-mobile\" style=\"background-image: url(https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-content\/uploads\/sites\/13\/2023\/11\/Tupperware.png?v=0.74);\"><\/div>\n    \t<div class=\"overlay\"><\/div>\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t\t<div class=\"hero-content\">\n\t\t\t    \t\t\t\t    <span class=\"section-title\">Az \u00e9let bonyolult, ha nincsenek meg a sz\u00fcks\u00e9ges eszk\u00f6z\u00f6k<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t    <h1>MI A PKU?\n<\/h1>\n\t\t\t\t\t\t\t\t\t\t\t\t    <p>A megk\u00e9rdezettek k\u00f6z\u00fcl 10-b\u0151l csak 1 hallott a PKU-r\u00f3l!<sup>12<\/sup><\/p>\n<p>A fenilketonuria (PKU) egy ritka, eg\u00e9sz \u00e9len \u00e1t tart\u00f3 anyagcsere rendelleness\u00e9g, amelynek k\u00f6vetkezt\u00e9ben a beteg csak korl\u00e1tozottan k\u00e9pes a feh\u00e9rj\u00e9t lebontani, \u00e9s amely kumulat\u00edv toxikus hat\u00e1sokat id\u00e9zhet el\u0151 az agyban<sup>1<\/sup>.<\/p>\n<p>A PKU betegs\u00e9ggel az elfogyasztott \u00e9tel k\u00f6zvetlen\u00fcl befoly\u00e1solja az agym\u0171k\u00f6d\u00e9s m\u00f3dj\u00e1t.<\/p>\n\t\t\t\t\t\t\t\t\n                <p class=\"inline-buttons\">\n                                                        <\/p>\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n<div id=\"acf-block-6548ddf13e044\" class=\"block split-content equal-bias\" data-muted-autoplay=\"false\">\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t                                                                <div class=\"content-block first-block\">\n                                                                                                                                                                                                                                                                                    \n                                    \n                                                                                                                \n                                    \n                                    <figure>\n                                        <div class=\"image image-rounded\">\n                                                                                            <img decoding=\"async\" class=\"\" src=\"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-content\/uploads\/sites\/13\/2023\/11\/Foodyoueat.png?v=0.74\" alt=\"Photo of green veg on dark kitchen surface\" \/>                                                                                    <\/div>\n                                                                            <\/figure>\n                                                                                    <\/div>\n                    \n                                            <div class=\"content-block second-block\">\n                                                                                                <p>A PKU-val \u00e9l\u0151knek a fenilalanin hidroxil\u00e1z (PAH) enzim okozza a neh\u00e9zs\u00e9get, ez\u00e9rt nem tudnak teljesen lebontani egy fenilalanin (Phe) nev\u0171 amin\u00f3savat, amely minden feh\u00e9rjetartalm\u00fa \u00e9telben (pl. di\u00f3f\u00e9l\u00e9k, h\u00fas, toj\u00e1s, tejterm\u00e9kek) \u00e9s az \u00e9des\u00edt\u0151kben, pl. az aszpartam1-ben is jelen van.<\/p>\n<p>T\u00falzott mennyis\u00e9g\u0171 feh\u00e9rje fogyaszt\u00e1sa eset\u00e9n nagy mennyis\u00e9g\u0171 Phe halmoz\u00f3dik fel a beteg v\u00e9r\u00e9ben, \u00e9s felbor\u00edtja a neurotranszmitterek egyens\u00faly\u00e1t, vagy ak\u00e1r fizikai k\u00e1rosod\u00e1st is okoz mag\u00e1ban az agyban. Ez olyan neurol\u00f3giai t\u00fcneteket is eredm\u00e9nyezhet, mint a mem\u00f3ri\u00e1val \u00e9s figyelemmel kapcsolatos probl\u00e9m\u00e1k, depresszi\u00f3 \u00e9s szorong\u00e1s<sup>2<\/sup>.<\/p>\n                                                                                    <\/div>\n                                                \t\t<\/div>\n\t<\/div>\n<\/div>\n\n<div id=\"acf-block-6548ddf13e102\" class=\"block split-content equal-bias bg-band bg-band-primary\" data-muted-autoplay=\"false\">\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t                                                                <div class=\"content-block first-block\">\n                                                                                                <h2><strong>A rendelleness\u00e9get \u2013 amely Eur\u00f3p\u00e1ban 10000 emberb\u0151l 1-et \u00e9rint<sup>1,3<\/sup>\u00a0\u2013 \u00fajsz\u00fcl\u00f6tteken az \u00fan. saroksz\u00far\u00e1s teszttel sz\u0171rik.<\/strong><\/h2>\n                                                                                    <\/div>\n                    \n                                            <div class=\"content-block second-block\">\n                                                                                                                                                                                                                                                                                    \n                                    \n                                                                                                                \n                                    \n                                    <figure>\n                                        <div class=\"image image-rounded\">\n                                                                                            <img decoding=\"async\" class=\"\" src=\"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-content\/uploads\/sites\/13\/2024\/02\/baby-foot.jpg?v=0.74\" alt=\"new-born heel prick test\" \/>                                                                                    <\/div>\n                                                                            <\/figure>\n                                                                                    <\/div>\n                                                \t\t<\/div>\n\t<\/div>\n<\/div>\n\n<div id=\"acf-block-6548ddf13e2e5\" class=\"block wrapped-content block-tight-top\">\n    <div class=\"wrapper\">\n        <div class=\"inner-wrapper\">\n                \n<div id=\"acf-block-6548ddf13e44a\" class=\"block-wysiwyg\">\n            <h3>A PKU \u00f6r\u00f6kl\u00f6tt autoszom\u00e1lis recessz\u00edv betegs\u00e9g. Ez azt jelenti, hogy ha mindk\u00e9t sz\u00fcl\u0151ben megvan a PKU g\u00e9n, akkor csecsem\u0151j\u00fck 1:4 es\u00e9llyel PKU<sup>4<\/sup>-gyel sz\u00fcletik. A rendelleness\u00e9get szinte minden eur\u00f3pai orsz\u00e1gban sz\u0171rik az \u00fajsz\u00fcl\u00f6tteken v\u00e9gzett saroksz\u00far\u00f3 teszttel, azonban a probl\u00e9m\u00e1ra \u00e1ltal\u00e1noss\u00e1gban kis figyelem ir\u00e1nyul.<\/h3>\n    <\/div>\n        <\/div>\n    <\/div>\n<\/div>\n\n<div id=\"acf-block-6548ddf13e4fd\" class=\"block split-content equal-bias\" data-muted-autoplay=\"false\">\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t                                                                <div class=\"content-block first-block\">\n                                                                                                <h2>A PKU jelenleg nem gy\u00f3gy\u00edthat\u00f3, \u00e9s kezel\u00e9se eg\u00e9sz \u00e9leten \u00e1t tart.<\/h2>\n<p>A k\u00f6zelm\u00faltig az orvosok azt hitt\u00e9k, hogy a PKU olyan rendelleness\u00e9g, amelyet tizen\u00e9ves korban a beteg kin\u0151, amint az agy teljes eg\u00e9sz\u00e9ben kifejl\u0151dik. Ma m\u00e1r tudjuk azonban, hogy a v\u00e9r magas Phe szintje tov\u00e1bbra is k\u00e1rosod\u00e1st okozhat b\u00e1rmely \u00e9letkorban, \u00edgy a probl\u00e9ma eg\u00e9sz \u00e9leten \u00e1t kezel\u00e9st ig\u00e9nyel<sup>5<\/sup>.<\/p>\n<p>Igen szigor\u00fa \u00e9trend \u00e9s\/vagy orvosi kezel\u00e9s sz\u00fcks\u00e9ges a Phe szint megfelel\u0151 szab\u00e1lyoz\u00e1s\u00e1hoz, \u00e9s hatalmas terhet r\u00f3 feln\u0151ttekre, amely \u00e9letmin\u0151s\u00e9g\u00fcket, \u00edgy szem\u00e9lyes kapcsolataikat is befoly\u00e1solja, \u00e9s hozz\u00e1j\u00e1rul a szorong\u00e1s, stessz \u00e9s depresszi\u00f3 kialakul\u00e1s\u00e1hoz\u00a0<sup>6,7<\/sup>.<\/p>\n                                                                                    <\/div>\n                    \n                                            <div class=\"content-block second-block\">\n                                                                                                                                                                                                                                                                                    \n                                    \n                                                                                                                \n                                    \n                                    <figure>\n                                        <div class=\"image image-rounded\">\n                                                                                            <img decoding=\"async\" class=\"\" src=\"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-content\/uploads\/sites\/13\/2023\/11\/AdobeStock_428548283-scaled-1-1900x1266.jpeg\" alt=\"Woman reading product label in grocery store\" \/>                                                                                    <\/div>\n                                                                            <\/figure>\n                                                                                    <\/div>\n                                                \t\t<\/div>\n\t<\/div>\n<\/div>\n\n<div id=\"acf-block-6582ff8310609\" class=\"block split-content equal-bias bg-band bg-band-primary\" data-muted-autoplay=\"false\">\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t                                                                <div class=\"content-block first-block\">\n                                                                                                <h2>A kezeletlen vagy rosszul kezelt PKU komoly k\u00f6vetkezm\u00e9nyekkel j\u00e1rhat.<\/h2>\n                                                                                    <\/div>\n                    \n                                            <div class=\"content-block second-block\">\n                                                                                                <p>A magas vagy instabil Phe szint az al\u00e1bbi k\u00f6vetkezm\u00e9nnyel j\u00e1rhat8,9:<\/p>\n<ul>\n<li><strong>Lass\u00fa inform\u00e1ci\u00f3 feldolgoz\u00e1s<\/strong><\/li>\n<li><strong>Viselked\u00e9si vagy szoci\u00e1lis probl\u00e9m\u00e1k<\/strong><\/li>\n<li><strong>Szellemi fogyat\u00e9koss\u00e1g<\/strong><\/li>\n<li><strong>Mem\u00f3ria probl\u00e9m\u00e1k<\/strong><\/li>\n<li><strong>Rohamok \u00e9s remeg\u00e9s<\/strong><\/li>\n<li><strong>Figyelemzavar<\/strong><\/li>\n<li><strong>Szorong\u00e1s, depresszi\u00f3 \u00e9s ingerl\u00e9kenys\u00e9g<\/strong><\/li>\n<\/ul>\n<p>A PKU-val \u00e9l\u0151k nagysz\u00e1m\u00fa testi komorbidit\u00e1s kock\u00e1zat\u00e1val is szembes\u00fclnek: elh\u00edz\u00e1s, magas v\u00e9rnyom\u00e1ssal p\u00e1rosul\u00f3 veseel\u00e9gtelens\u00e9g \u00e9s csontritkul\u00e1s<sup>10<\/sup>.<\/p>\n                                                                                    <\/div>\n                                                \t\t<\/div>\n\t<\/div>\n<\/div>\n\n<div id=\"acf-block-6582fc1798f20\" class=\"block wrapped-content block-tight-top\">\n    <div class=\"wrapper\">\n        <div class=\"inner-wrapper\">\n                \n<div id=\"acf-block-6582fd84e0f26\" class=\"block-wysiwyg\">\n            <h2>A PKU-val \u00e9l\u0151 feln\u0151tteknek gyakran szigor\u00fa \u00e9trend szerint kell t\u00e1pl\u00e1lkozniuk.<\/h2>\n    <\/div>\n        <\/div>\n    <\/div>\n<\/div>\n\n<div id=\"acf-block-6582fd84e1b41\" class=\"block split-content equal-bias bottom-border\" data-muted-autoplay=\"false\">\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t                                                                <div class=\"content-block first-block\">\n                                                                                                <p>A Phe szint kontroll\u00e1l\u00e1s\u00e1hoz sz\u00fcks\u00e9ges \u00e9trend k\u00f6vet\u00e9se gondos tervez\u00e9st ig\u00e9nyel. Azonban mag\u00e1nak a PKU-nak a neurokognit\u00edv hat\u00e1sai ezt m\u00e9g nehezebb\u00e9 tehetik. Ezt pedig m\u00e9g tov\u00e1bb ronthatja az \u00e9trend k\u00f6vet\u00e9s\u00e9nek fegyelmezetlens\u00e9ge, amely \u00edgy \u00f6rd\u00f6gi k\u00f6rt jelent a PKU-val \u00e9l\u0151k sz\u00e1m\u00e1ra<sup>7,9<\/sup>.<\/p>\n<p>18 \u00e9ves kor f\u00f6l\u00f6tt gyakori, hogy az \u00e9rintettek kev\u00e9sb\u00e9 tartj\u00e1k k\u00e9zben PKU-jukat. Ezt val\u00f3sz\u00edn\u0171leg t\u00f6bb t\u00e9nyez\u0151 is magyar\u00e1zza, \u00edgy pl. a t\u00f6bb elfoglalts\u00e1g, a PKU-hoz igazod\u00f3 \u00e9lelmiszer rendelkez\u00e9sre \u00e1ll\u00e1sa k\u00f6z\u00f6ss\u00e9gi egy\u00fcttl\u00e9tek alkalm\u00e1val, illetve kevesebb olyan szakrendel\u0151, ahol feln\u0151tteket is kezelnek<sup>11<\/sup>.<\/p>\n<p>M\u00e9g ha a PKU-val \u00e9l\u0151k szigor\u00faan be is tartj\u00e1k az el\u0151\u00edrt \u00e9trendet, az kedvez\u0151tlen hat\u00e1ssal lehet \u00e9let\u00fck egy\u00e9b ter\u00fclet\u00e9re: 34% azt jelezte vissza, hogy bar\u00e1taival, csal\u00e1dj\u00e1val vagy partner\u00e9vel val\u00f3 kapcsolat\u00e1t nehez\u00edti a betegs\u00e9g, \u00e9s 44% \u00e1ll\u00edt\u00e1sa szerint t\u00e1rsadalmi kirekesztetts\u00e9get tapasztal<sup>7<\/sup>.<\/p>\n<p><a href=\"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/minek-kell-megvaltoznia\/\">Tudjon meg t\u00f6bbet arr\u00f3l, amit az \u00c9lj teljes \u00e9letet PKU kamp\u00e1ny tesz a v\u00e1ltoz\u00e1sok el\u0151seg\u00edt\u00e9se \u00e9rdek\u00e9ben.<\/a><\/p>\n                                                                                    <\/div>\n                    \n                                            <div class=\"content-block second-block\">\n                                                                                                                                                                                                                                                                                    \n                                    \n                                                                                                                \n                                    \n                                    <figure>\n                                        <div class=\"image image-rounded\">\n                                                                                            <img decoding=\"async\" class=\"\" src=\"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-content\/uploads\/sites\/13\/2023\/12\/hannah-olinger-NXiIVnzBwZ8-unsplash-B.png?v=0.74\" alt=\"\" \/>                                                                                    <\/div>\n                                                                            <\/figure>\n                                                                                    <\/div>\n                                                \t\t<\/div>\n\t<\/div>\n<\/div>\n\n<div id=\"acf-block-6548ddf13e901\" class=\"block references\">\n    <div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t    \t\t\t    <h4><strong>Referenci\u00e1k<\/strong>:\n<\/h4>\n\t\t\t\t\t\t                <ol>\n                                                                                                                        <li><span>Wegberg AMJ, MacDonald A, Ahring K \u00e9s m\u00e1sok. The complete European guidelines on phenylketonuria: diagnosis and treatment. (A fenilketonuri\u00e1val kapcsolatos \u00f6sszes Eur\u00f3pai Ir\u00e1nyelv) Orphanet J Rare Dis. 2017;12(1):162. 2017 okt\u00f3ber Orphanet J Rare Dis. 2017;12(1):162. Kiadva: 2017. okt. 12. doi:10.1186\/s13023-017-0685-2.\n<\/span><\/li>\n                                                                                                                                                <li><span>Bilder DA \u00e9s m\u00e1sok. Systematic Review and Meta-Analysis of Neuropsychiatric Symptoms and Executive Functioning in Adults With Phenylketonuria. (Neuropszichi\u00e1triai t\u00fcnetek k\u00f6vetkezetes \u00e1ttekint\u00e9se \u00e9s meta-elemz\u00e9se \u00e9s a v\u00e9grehajt\u00f3 funkci\u00f3k fenilketonuri\u00e1val \u00e9l\u0151 feln\u0151ttekn\u00e9l) Dev Neuropsychol. 2016. m\u00e1jus-j\u00fanius;41(4):245-260.\n<\/span><\/li>\n                                                                                                                                                <li><span>Pitt, J. Newborn Screening. (\u00dajsz\u00fcl\u00f6ttek sz\u0171r\u00e9se) Clin Biochem Rev. 2010 May; 31(2): 57\u201368.\n<\/span><\/li>\n                                                                                                                                                <li><span>NORD. 2019. Phenylketonuria. (Fenilketonuria) El\u00e9rhet\u0151 a k\u00f6vetkez\u0151 hivatkoz\u00e1son: https:\/\/rarediseases.org\/rare-diseases\/phenylketonuria\/. Utols\u00f3 hozz\u00e1f\u00e9r\u00e9s 2019. \u00e1prilis\n<\/span><\/li>\n                                                                                                                                                <li><span>Berry \u00e9s m\u00e1sok. Newborn screening 50 years later: access issues faced by adults with PKU. Genetics in Medicine (\u00dajsz\u00fcl\u00f6ttek sz\u0171r\u00e9se 50 \u00e9vvel k\u00e9s\u0151bb: PKU-val \u00e9l\u0151 feln\u0151ttek neh\u00e9zs\u00e9gei a kezel\u00e9shez val\u00f3 hozz\u00e1f\u00e9r\u00e9ssel. Genetika az orvostanban) 15. k\u00f6tet, 591\u2013599. old. (2013)\n<\/span><\/li>\n                                                                                                                                                <li><span>Al Hafid N, Christodoulou J. Phenylketonuria: a review of current and future treatments. (Fenilketonuria: jelen \u00e9s j\u00f6v\u0151beli kezel\u00e9sek \u00e1ttekint\u00e9se) Transl Pediatr. 2015;4(4):304\u2013317. doi:10.3978\/j.issn.2224-4336.2015.10.07\n<\/span><\/li>\n                                                                                                                                                <li><span>Ford, S. \u00e9s m\u00e1sok. Living with Phenylketonuria: Lessons from the PKU community. Molecular Genetics and Metabolism Report. (Fenilketonuri\u00e1val \u00e9lni: a PKU k\u00f6z\u00f6ss\u00e9gt\u0151l kapott lecke. Molekul\u00e1ris genetika \u00e9s metabolizmus jelent\u00e9s) 2018\n<\/span><\/li>\n                                                                                                                                                <li><span>BioMarin Pharmaceuticals. 2017.Phe In The Brain (Phe az agyban) | PKU. Phenylketonuria (PKU) Information [ONLINE]. El\u00e9rhet\u0151 a k\u00f6vetkez\u0151 hivatkoz\u00e1son: http:\/\/www.pku.com\/about-pku\/phe-in-the-brain. Utolj\u00e1ra lek\u00e9rdezve: 2019. \u00e1prilis\n<\/span><\/li>\n                                                                                                                                                <li><span>BioMarin Pharmaceuticals. 2019. PKU. [ONLINE] El\u00e9rhet\u0151 a k\u00f6vetkez\u0151 hivatkoz\u00e1son: https:\/\/www.biomarin.com\/patients\/ diseases\/pku. Utolj\u00e1ra lek\u00e9rdezve: April 2019\n<\/span><\/li>\n                                                                                                                                                <li><span>Burton, B., Jones, K., Cederbaum, S., Rohr, F., Waisbren, S., Irwin, D., Kim, G., Lilienstein, J., Alvarez, I., Jurecki, E. \u00e9s Levy, H. (2018). Prevalence of comorbid conditions among adult patients diagnosed with phenylketonuria. Molecular Genetics and Metabolism, 125(3), (A komorbid \u00e1llapotok elterjedts\u00e9ge fenilketonuri\u00e1val diagnosztiz\u00e1lt feln\u0151tt betegek k\u00f6r\u00e9ben. Molekul\u00e1ris genetika \u00e9s metabolizmus, 125(3) pp.228-234.\n<\/span><\/li>\n                                                                                                                                                <li><span>Cazzorla C et Al. Living with phenylketonuria in adulthood: The PKU ATTITUDE study. Molecular Genetics and Metabolism Reports 16 (Fenilketonuri\u00e1val \u00e9lni feln\u0151ttkorban: A PKU MAGATART\u00c1S. Molekul\u00e1ris genetika \u00e9s metabolizmus jelent\u00e9sek) (2018) 39\u201345\n<\/span><\/li>\n                                                                                                                                                <li><span>A BioMarin megb\u00edzta az Alligator k\u00f6zv\u00e9lem\u00e9nykutat\u00f3 c\u00e9get egy hat k\u00e9rd\u00e9sb\u0151l \u00e1ll\u00f3 online felm\u00e9r\u00e9s elk\u00e9sz\u00edt\u00e9s\u00e9vel az Egyes\u00fclt Kir\u00e1lys\u00e1g, Franciaorsz\u00e1g, N\u00e9metorsz\u00e1g, Olaszorsz\u00e1g, Spanyolorsz\u00e1g, Sv\u00e9dorsz\u00e1g, Hollandia \u00e9s T\u00f6r\u00f6korsz\u00e1g orsz\u00e1gosan reprezentat\u00edv mint\u00e1i alapj\u00e1n \u00f6sszesen 4151 v\u00e1laszad\u00f3val.* A felm\u00e9r\u00e9sre 2019. j\u00fanius 1. \u00e9s 6. k\u00f6z\u00f6tt ker\u00fclt sor. A v\u00e1laszad\u00f3kat arra k\u00e9rt\u00fck, hogy \u00e9let\u00fck hat m\u00e9rf\u00f6ldk\u00f6v\u00e9t \u00e9rt\u00e9kelj\u00e9k 5 fokozat\u00fa sk\u00e1l\u00e1n (\u201eegy\u00e1ltal\u00e1n nem\u201d jelent stresszt \u2013 \u201erendk\u00edv\u00fcli\u201d stresszt jelent). Valamilyen eg\u00e9szs\u00e9g\u00fcgyi probl\u00e9m\u00e1val rendelkez\u0151 v\u00e1laszad\u00f3k \u00f6sszesen: 1932. \u00d6sszesen 112 PKU beteget kerest\u00fcnk meg k\u00fcl\u00f6n-k\u00fcl\u00f6n olaszorsz\u00e1gi, sv\u00e9dorsz\u00e1gi, spanyolorsz\u00e1gi, t\u00f6r\u00f6korsz\u00e1gi \u00e9s hollandiai betegcsoportokkal egy\u00fcttm\u0171k\u00f6dve.\n<\/span><\/li>\n                                                            <\/ol>\n\t\t\t\t\t<\/div>\n\t<\/div>\n<\/div>","protected":false},"excerpt":{"rendered":"","protected":false},"author":2,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"inline_featured_image":false,"footnotes":""},"class_list":["post-51","page","type-page","status-publish","hentry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Mia PKU? | Live Unlimited PKU<\/title>\n<meta name=\"description\" content=\"A PKU seg\u00edts\u00e9g\u00e9vel az elfogyasztott \u00e9tel befoly\u00e1solhatja az agy m\u0171k\u00f6d\u00e9s\u00e9t. Jelenleg nincs gy\u00f3gym\u00f3d a PKU-ra, \u00e9s a betegs\u00e9g kezel\u00e9s\u00e9nek \u00e9lethosszig tart\u00f3nak kell lennie.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/mi-a-pku\/\" \/>\n<meta property=\"og:locale\" content=\"hu_HU\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Mia PKU? | Live Unlimited PKU\" \/>\n<meta property=\"og:description\" content=\"A PKU seg\u00edts\u00e9g\u00e9vel az elfogyasztott \u00e9tel befoly\u00e1solhatja az agy m\u0171k\u00f6d\u00e9s\u00e9t. Jelenleg nincs gy\u00f3gym\u00f3d a PKU-ra, \u00e9s a betegs\u00e9g kezel\u00e9s\u00e9nek \u00e9lethosszig tart\u00f3nak kell lennie.\" \/>\n<meta property=\"og:url\" content=\"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/mi-a-pku\/\" \/>\n<meta property=\"og:site_name\" content=\"BioMarin Live Unlimited HU-HU\" \/>\n<meta property=\"article:modified_time\" content=\"2024-12-07T20:24:57+00:00\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/pku.biomarin.com\\\/hu-hu\\\/liveunlimited\\\/mi-a-pku\\\/\",\"url\":\"https:\\\/\\\/pku.biomarin.com\\\/hu-hu\\\/liveunlimited\\\/mi-a-pku\\\/\",\"name\":\"Mia PKU? | Live Unlimited PKU\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/pku.biomarin.com\\\/hu-hu\\\/liveunlimited\\\/#website\"},\"datePublished\":\"2023-11-06T10:45:02+00:00\",\"dateModified\":\"2024-12-07T20:24:57+00:00\",\"description\":\"A PKU seg\u00edts\u00e9g\u00e9vel az elfogyasztott \u00e9tel befoly\u00e1solhatja az agy m\u0171k\u00f6d\u00e9s\u00e9t. Jelenleg nincs gy\u00f3gym\u00f3d a PKU-ra, \u00e9s a betegs\u00e9g kezel\u00e9s\u00e9nek \u00e9lethosszig tart\u00f3nak kell lennie.\",\"breadcrumb\":{\"@id\":\"https:\\\/\\\/pku.biomarin.com\\\/hu-hu\\\/liveunlimited\\\/mi-a-pku\\\/#breadcrumb\"},\"inLanguage\":\"hu\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\\\/\\\/pku.biomarin.com\\\/hu-hu\\\/liveunlimited\\\/mi-a-pku\\\/\"]}]},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\\\/\\\/pku.biomarin.com\\\/hu-hu\\\/liveunlimited\\\/mi-a-pku\\\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\\\/\\\/pku.biomarin.com\\\/hu-hu\\\/liveunlimited\\\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Mi a PKU?\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\\\/\\\/pku.biomarin.com\\\/hu-hu\\\/liveunlimited\\\/#website\",\"url\":\"https:\\\/\\\/pku.biomarin.com\\\/hu-hu\\\/liveunlimited\\\/\",\"name\":\"BioMarin Live Unlimited HU-HU\",\"description\":\"\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\\\/\\\/pku.biomarin.com\\\/hu-hu\\\/liveunlimited\\\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"hu\"}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Mia PKU? | Live Unlimited PKU","description":"A PKU seg\u00edts\u00e9g\u00e9vel az elfogyasztott \u00e9tel befoly\u00e1solhatja az agy m\u0171k\u00f6d\u00e9s\u00e9t. Jelenleg nincs gy\u00f3gym\u00f3d a PKU-ra, \u00e9s a betegs\u00e9g kezel\u00e9s\u00e9nek \u00e9lethosszig tart\u00f3nak kell lennie.","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/mi-a-pku\/","og_locale":"hu_HU","og_type":"article","og_title":"Mia PKU? | Live Unlimited PKU","og_description":"A PKU seg\u00edts\u00e9g\u00e9vel az elfogyasztott \u00e9tel befoly\u00e1solhatja az agy m\u0171k\u00f6d\u00e9s\u00e9t. Jelenleg nincs gy\u00f3gym\u00f3d a PKU-ra, \u00e9s a betegs\u00e9g kezel\u00e9s\u00e9nek \u00e9lethosszig tart\u00f3nak kell lennie.","og_url":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/mi-a-pku\/","og_site_name":"BioMarin Live Unlimited HU-HU","article_modified_time":"2024-12-07T20:24:57+00:00","twitter_card":"summary_large_image","schema":{"@context":"https:\/\/schema.org","@graph":[{"@type":"WebPage","@id":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/mi-a-pku\/","url":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/mi-a-pku\/","name":"Mia PKU? | Live Unlimited PKU","isPartOf":{"@id":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/#website"},"datePublished":"2023-11-06T10:45:02+00:00","dateModified":"2024-12-07T20:24:57+00:00","description":"A PKU seg\u00edts\u00e9g\u00e9vel az elfogyasztott \u00e9tel befoly\u00e1solhatja az agy m\u0171k\u00f6d\u00e9s\u00e9t. Jelenleg nincs gy\u00f3gym\u00f3d a PKU-ra, \u00e9s a betegs\u00e9g kezel\u00e9s\u00e9nek \u00e9lethosszig tart\u00f3nak kell lennie.","breadcrumb":{"@id":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/mi-a-pku\/#breadcrumb"},"inLanguage":"hu","potentialAction":[{"@type":"ReadAction","target":["https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/mi-a-pku\/"]}]},{"@type":"BreadcrumbList","@id":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/mi-a-pku\/#breadcrumb","itemListElement":[{"@type":"ListItem","position":1,"name":"Home","item":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/"},{"@type":"ListItem","position":2,"name":"Mi a PKU?"}]},{"@type":"WebSite","@id":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/#website","url":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/","name":"BioMarin Live Unlimited HU-HU","description":"","potentialAction":[{"@type":"SearchAction","target":{"@type":"EntryPoint","urlTemplate":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/?s={search_term_string}"},"query-input":{"@type":"PropertyValueSpecification","valueRequired":true,"valueName":"search_term_string"}}],"inLanguage":"hu"}]}},"_links":{"self":[{"href":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-json\/wp\/v2\/pages\/51","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-json\/wp\/v2\/comments?post=51"}],"version-history":[{"count":119,"href":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-json\/wp\/v2\/pages\/51\/revisions"}],"predecessor-version":[{"id":1454,"href":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-json\/wp\/v2\/pages\/51\/revisions\/1454"}],"wp:attachment":[{"href":"https:\/\/pku.biomarin.com\/hu-hu\/liveunlimited\/wp-json\/wp\/v2\/media?parent=51"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}