{"id":1467,"date":"2023-02-24T17:37:40","date_gmt":"2023-02-24T17:37:40","guid":{"rendered":"https:\/\/pku.biomarin.com\/de-de\/?page_id=1467"},"modified":"2024-08-26T20:12:07","modified_gmt":"2024-08-26T20:12:07","slug":"pku-leitlinien-und-standards","status":"publish","type":"page","link":"https:\/\/pku.biomarin.com\/de-de\/pku-leitlinien-und-standards\/","title":{"rendered":"PKU Leitlinien &amp; Standards"},"content":{"rendered":"<div id=\"acf-block-63f8f80914b60\" class=\"hero hero-no-overlay\">\n            <div class=\"hero-background-image hero-background-image-desktop\" style=\"background-image: url(https:\/\/pku.biomarin.com\/de-de\/wp-content\/uploads\/sites\/12\/2023\/03\/Group-110-scaled-e1678703759379-2000x435.jpg);\"><\/div>\n\t    <div class=\"hero-background-image hero-background-image-mobile\" style=\"background-image: url(https:\/\/pku.biomarin.com\/de-de\/wp-content\/uploads\/sites\/12\/2023\/02\/pku-balloon-hero-mobile-830x800.jpg);\"><\/div>\n    \t<div class=\"overlay\"><\/div>\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t\t<div class=\"hero-content\">\n\t\t\t    \t\t\t\t\t\t\t\t\t\t\t\t    <h1>PKU Leitlinien &amp; Standards\n<\/h1>\n\t\t\t\t\t\t\t\t\t\t\t\t\n                <p class=\"inline-buttons\">\n                                                        <\/p>\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n<div id=\"acf-block-63f8f80914cf0\" class=\"block wrapped-content block-tight-bottom\">\n    <div class=\"wrapper\">\n        <div class=\"inner-wrapper\">\n                \n<div id=\"acf-block-63f8f80914dfd\" class=\"block-wysiwyg\">\n            <h2>PKU-Experten empfehlen f\u00fcr alle Personen mit PKU eine lebenslange medizinische Betreuung<\/h2>\n<p>Eine Gruppe von PKU-Spezialisten hat Leitlinien erarbeitet, die \u00c4rzte bei der Behandlung von Personen mit PKU unterst\u00fctzen sollen.<\/p>\n    <\/div>\n        <\/div>\n    <\/div>\n<\/div>\n\n<div id=\"acf-block-63f8f8091694f\" class=\"block split-content equal-bias bottom-border\" data-muted-autoplay=\"false\">\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t                                                                <div class=\"content-block first-block\">\n                                                                                                                                                                                                                                                                                    \n                                    \n                                                                                                                \n                                    \n                                    <figure>\n                                        <div class=\"image image-rounded\">\n                                                                                            <img decoding=\"async\" class=\"\" src=\"https:\/\/pku.biomarin.com\/de-de\/wp-content\/uploads\/sites\/12\/2023\/02\/1.2_Desktop_Treatment_guidelines.jpg?v=0.85\" alt=\"\" \/>                                                                                    <\/div>\n                                                                            <\/figure>\n                                                                                    <\/div>\n                    \n                                            <div class=\"content-block second-block\">\n                                                                                                <h3>Diesen Leitlinien zufolge sollten Personen mit PKU:<\/h3>\n<p><strong>Fr\u00fchzeitig mit der PKU-Behandlung beginnen.<\/strong> Die PKU-Behandlung sollte innerhalb der ersten 10 Lebenstage begonnen werden.<\/p>\n<p><strong>PKU lebenslang behandeln.<\/strong> Die PKU ist eine lebenslange Erkrankung, die eine lebenslange Behandlung erfordert.<\/p>\n<p><strong>Phe-Spiegel im empfohlenen Bereich halten.<\/strong> Die Menge an Phe, die im Rahmen einer PKU-Di\u00e4t aufgenommen wird, muss \u00fcberwacht werden und ist bei jeder Person mit PKU unterschiedlich. Experten empfehlen, den Phe-Spiegel im Blut bei Kindern unter 12 Jahren und Schwangeren zwischen 120 und 360 \u00b5mol\/l (2 &#8211; 6 mg\/dl) und bei Personen \u00fcber 12 Jahren zwischen 120 und 600 \u00b5mol\/l (2 &#8211; 10 mg\/dl) zu halten.<\/p>\n<p><strong>Behandlung wieder aufnehmen.<\/strong> Es ist nie zu sp\u00e4t, die PKU zu behandeln. Personen mit PKU, die die Behandlung wieder aufnehmen, werden m\u00f6glicherweise eine Besserung ihrer Symptome feststellen.<\/p>\n                                                                                    <\/div>\n                                                \t\t<\/div>\n\t<\/div>\n<\/div>\n\n<div id=\"acf-block-63f8f80916ba7\" class=\"block cards cards-2-col block-tight-top\">\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t\t<div class=\"cards-title\">\n\t\t\t    \t\t\t\t\t\t\t<\/div>\n\t\t\t<div class=\"cards-wrapper\">\n\t\t\t    \n<div id=\"acf-block-63f8f8091700d\" class=\"card card-fixed-button\" data-muted-autoplay=\"false\">\n    \t    \n\n                    <img decoding=\"async\" class=\"card-image\" src=\"https:\/\/pku.biomarin.com\/de-de\/wp-content\/uploads\/sites\/12\/2024\/01\/5.2_Desktop_StoryFlowCTA1@4xB.png?v=0.85\" alt=\"\" \/>        \n\t    <div class=\"card-content\">\n                            <h4>Wie die PKU Ihr Denken, F\u00fchlen und Handeln beeinflusst\n<\/h4>\n        \n                                                                                                                                                                                                                                                                                    \n                                                                                        <\/div>\n                                <div class=\"card-actions\">\n                            \n                            <p><a class=\"button button-arrow\" href=\"https:\/\/pku.biomarin.com\/de-de\/phe-im-gehirn\/\" target=\"_self\">Mehr \u00fcber Phe erfahren<\/a><\/p>\n                                                                                    <\/div>\n<\/div>\n\n<div id=\"acf-block-63f8f80917098\" class=\"card card-fixed-button\" data-muted-autoplay=\"false\">\n    \t    \n\n                    <img decoding=\"async\" class=\"card-image\" src=\"https:\/\/pku.biomarin.com\/de-de\/wp-content\/uploads\/sites\/12\/2024\/01\/desktop_CTAblock_Icon2@4xB.png?v=0.85\" alt=\"\" \/>        \n\t    <div class=\"card-content\">\n                            <h4>Wie Sie Ihren Phe-Blutspiegel niedrig halten k\u00f6nnen\n<\/h4>\n        \n                                                                                                                                                                                                                                                                                    \n                                                                                        <\/div>\n                                <div class=\"card-actions\">\n                            \n                            <p><a class=\"button button-arrow\" href=\"https:\/\/pku.biomarin.com\/de-de\/behandlung-der-pku\/\" target=\"_self\">Behandlung der PKU<\/a><\/p>\n                                                                                    <\/div>\n<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>","protected":false},"excerpt":{"rendered":"","protected":false},"author":3,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"inline_featured_image":false,"footnotes":""},"class_list":["post-1467","page","type-page","status-publish","hentry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>PKU Leitlinien &amp; 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